Table 1 Demographic and clinical characteristics of included patients with Susac Syndrome
Demographic characteristics | Clinical signs of Susac syndrome | Therapy*** | ||||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Patient | Sex [m = male; f = female] | Age at disease onset | Age at diagnosis | Age at MRI** | Encephalopathy [yes = 1; no = 0] | BRAO* [yes = 1; no = 0] | Labyrinthine deafness [yes = 1; no = 0] | Disease activity at MRI** [active = 1; stable = 0] | Comorbidities | Past | Current [0 = none] | |||
#1 | m | 32 | 33 | 40 | 1 | 1 | 1 | 0 | - | MP, PLEX, CYC, RTX, AZA | 0 | |||
#2 | f | 32 | 34 | 38 | 1 | 1 | 1 | 0 | - | MP, IVIG | 0 | |||
#3 | m | 24 | 26 | 42 | 1 | 1 | 1 | 0 | vitiligo, pernicious anemia, lichen sclerosus, chronic bronchitis, pyelonephritis | MP | 0 | |||
#4 | f | 29 | 30 | 37 | 1 | 1 | 1 | 0 | - | MP, IVIG, RTX | IVIG | |||
#5 | f | 18 | 18 | 22 | 1 | 1 | 1 | 0 | - | MP, IVIG | 0 | |||
#6 | f | 32 | 33 | 37 | 1 | 1 | 1 | 0 | - | RTX | 0 | |||
#7 | f | 34 | 35 | 46 | 1 | 1 | 1 | 0 | Hashimoto’s thyroiditis | MP, IVIG | 0 | |||