Fig. 4

Multiple associated anomalies. 14 years old, Marfan syndrome. Dilation of the aorta [black arrow (a)] and Valsalva sinus aneurysmal dilation [red arrows (b)]. Dilation of the pulmonary artery. Dorsal scoliosis (c) with thoracic deformation and hypoplasia of both lungs (d). Presence of a complete common mesentery; the small intestinal loops being located to the right of the colon [yellow arrow (e)]