From: Diagnostic accuracy of multi-slice computed tomography in children with Abernethy malformation
Case No. | Age (y)/Sex | Clinical Features | Fistula classification and anatomy | Treatment |
---|---|---|---|---|
1 | 11 years/Female | VSD, Hyperammonemia, Abnormal liver function | Type Ib(PV-IVC) | Lost to follow-up |
2 | 6 years/Female | PH, Nodular liver lesions | Type Ib(PV-IVC) | Liver transplantation |
3 | 12 years/Male | Hematochezia, PH, Hyperammonemia | Type Ib(SV-iliac vein-IVC) | Lost to follow-up |
4 | 11 years/Female | Cyanosis, Pulmonary arteriovenous fistula, Hyperammonemia | Type II(PV-IVC) | Surgical shunt occlusion |
5 | 9 years/Male | Fatigue, PDA, Nodular liver lesions | Type II(PV-IVC) | Surgical shunt occlusion |
6 | 4 years/Male | PH, Hyperammonemia | Type II(PV-IVC) | Surgical shunt occlusion |
7 | 9 years/Male | Fatigue, PH, Hepatic encephalopathy, Heart insufficiency, Hyperammonemia | Type II(PV-IVC) | Surgical shunt occlusion |
8 | 14 years/Male | Fatigue, VSD, Hyperammonemia, Nodular liver lesions | Type II(PV-IVC) | Lost to follow-up |
9 | 5 years/Male | Cyanosis, Pulmonary arteriovenous fistula, Hyperammonemia | Type II(PV-IVC) | Interventional portocaval shunt occlusion under DSA |
10 | 10 years/Female | Hematuria, Renal vascular malformation, Hyperammonemia | Type II(SV-iliac vein-IVC) | Surgical shunt occlusion |
11 | 3 years/Female | ASD,PH, Abnormal liver function | Type II(PV-IVC) | Interventional portocaval shunt occlusion under DSA |
12 | 4 years/Male | Fatigue, ASD/PAPVC, Pulmonary arteriovenous fistula, Hyperammonemia, PH | Type II(PV-LRV-IVC) | Surgical shunt occlusion |
13 | 7 years/Male | PH, Hyperammonemia | Type II(PV-IVC) | Surgical shunt occlusion |
14 | 1 year/Female | Cyanosis, ASD, Polysplenia syndrome, Pulmonary arteriovenous fistula | Type II(SMV-LRV-IVC) | Interventional portocaval shunt occlusion under DSA |