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Table 3 Clinical features of ALS patients

From: Tract integrity in amyotrophic lateral sclerosis: 6–month evaluation using MR diffusion tensor imaging

Subjects

Age

Gender

Handedness

El Escorial category

Phenotypea

Site of Onsetb

Riluzole

Disease duration (months)c

1

57

Male

Right

Definite

classic

RLL

Y

15

2

68

Male

Right

Definite

classic

LUL

N

27

3

74

Male

Right

Definite

atypical

RUL

N

48

4

63

Female

Left

Definite

classic

LLL

65

5

41

Male

Right

Definite

classic

RUL

Y

22

6

65

Female

Right

Definite

classic

LUL

N

17

7

51

Male

Right

Definite

slow progression

LL (Bilateral)

N

68

8

47

Male

Mixed

Definite

flail

LLL

Y

30

9

57

Male

Right

Definite

flail

LUL

Y

28

10

71

Male

Right

Definite

flail

RLL

Y

19

11

28

Female

Right

Definite

UMN

LUL

Y

13

12

54

Female

Right

Definite

slow progression

LUL

N

2.8

13

66

Female

Right

Definite

classic

RLL

Y

6

14

63

Male

Right

Definite

classic

RUL

N

8

15

60

Female

Right

Definite

classic

LLL

31

16

71

Male

Right

Definite

classic

RUL

N

112

17

52

Male

Right

Definite

atypical

LUL

Y

11

18

68

Male

Right

Definite

slow progression

LLL

N

14

19

60

Male

Right

Definite

classic

Bulbar

N

26

20

53

Male

Right

Definite

UMN

LL

Y

27

21

59

Male

Left

Definite

classic

RLL

N

11

22

60

Female

Left

Definite

classic

LLL

N

24

23

71

Male

Right

Definite

classic

Bulbar

N

16

  1. aPhenotype as described by Chio et al. 2011 [21]. Those patients with long survival hasve been designated as atypical
  2. bRUL: right upper limb, RLL: right lower limb, LUL: left upper limb, LLL: left lower limb, LL: lower limb
  3. cdisease duration is taken from the time of onset of symptoms until the time of the first scan