Subjects | Age | Gender | Handedness | El Escorial category | Phenotypea | Site of Onsetb | Riluzole | Disease duration (months)c |
---|---|---|---|---|---|---|---|---|
1 | 57 | Male | Right | Definite | classic | RLL | Y | 15 |
2 | 68 | Male | Right | Definite | classic | LUL | N | 27 |
3 | 74 | Male | Right | Definite | atypical | RUL | N | 48 |
4 | 63 | Female | Left | Definite | classic | LLL | – | 65 |
5 | 41 | Male | Right | Definite | classic | RUL | Y | 22 |
6 | 65 | Female | Right | Definite | classic | LUL | N | 17 |
7 | 51 | Male | Right | Definite | slow progression | LL (Bilateral) | N | 68 |
8 | 47 | Male | Mixed | Definite | flail | LLL | Y | 30 |
9 | 57 | Male | Right | Definite | flail | LUL | Y | 28 |
10 | 71 | Male | Right | Definite | flail | RLL | Y | 19 |
11 | 28 | Female | Right | Definite | UMN | LUL | Y | 13 |
12 | 54 | Female | Right | Definite | slow progression | LUL | N | 2.8 |
13 | 66 | Female | Right | Definite | classic | RLL | Y | 6 |
14 | 63 | Male | Right | Definite | classic | RUL | N | 8 |
15 | 60 | Female | Right | Definite | classic | LLL | – | 31 |
16 | 71 | Male | Right | Definite | classic | RUL | N | 112 |
17 | 52 | Male | Right | Definite | atypical | LUL | Y | 11 |
18 | 68 | Male | Right | Definite | slow progression | LLL | N | 14 |
19 | 60 | Male | Right | Definite | classic | Bulbar | N | 26 |
20 | 53 | Male | Right | Definite | UMN | LL | Y | 27 |
21 | 59 | Male | Left | Definite | classic | RLL | N | 11 |
22 | 60 | Female | Left | Definite | classic | LLL | N | 24 |
23 | 71 | Male | Right | Definite | classic | Bulbar | N | 16 |